TSHA-105 for SLC13A5 Deficiency

(SLC13A5 Trial)

TL
SM
Overseen BySouad Messahel, PhD
Age: < 65
Sex: Any
Trial Phase: Phase 1 & 2
Sponsor: TESS Research Foundation
No Placebo GroupAll trial participants will receive the active study treatment (no placebo)

What You Need to Know Before You Apply

What is the purpose of this trial?

This trial tests a new treatment called TSHA-105, an experimental therapy for individuals with SLC13A5 Citrate Transporter Disorder, a genetic condition affecting brain function. The study aims to determine if a single administration of this treatment into the spine is safe and effective. It seeks participants with this specific genetic disorder who exhibit related symptoms. As a Phase 1, Phase 2 trial, this research focuses on understanding how the treatment works in people and measuring its effectiveness in an initial, smaller group, offering participants a chance to contribute to groundbreaking research.

Will I have to stop taking my current medications?

The trial does not clearly state if you need to stop your current medications, but it mentions that if you have a chronic condition requiring ongoing medication, it might pose unnecessary risks for the study. It's best to discuss your specific medications with the trial team.

Is there any evidence suggesting that TSHA-105 is likely to be safe for humans?

Research shows that TSHA-105 is undergoing its first safety tests in humans. This gene therapy targets SLC13A5 deficiency, a condition that can cause seizures and developmental issues. Although human data is not yet available, animal studies have shown positive results, prompting human trials.

As an early-stage clinical trial, the safety of TSHA-105 in humans receives close monitoring. These initial trials focus on ensuring participant safety. While specific human data is not yet available, the trial's progress indicates confidence in its potential safety.

Participants will receive the treatment through an injection into the spinal canal, a common method for delivering gene therapies. As with any new treatment, side effects may occur, but these are still under study. The trial aims to gather clearer information on how well participants tolerate this treatment.12345

Why do researchers think this study treatment might be promising?

TSHA-105 is unique because it targets the underlying genetic cause of SLC13A5 deficiency, a rare disorder that affects brain metabolism. Unlike standard treatments that mainly address symptoms like seizures, TSHA-105 is designed to deliver a corrected version of the gene directly to the brain cells. This approach offers the potential to not just manage symptoms but to actually modify the disease itself, which is why researchers are excited about its possibilities.

What evidence suggests that TSHA-105 might be an effective treatment for SLC13A5 Deficiency?

Research has shown that TSHA-105, a gene therapy administered through the spinal fluid, appears promising in early studies. In mice lacking the SLC13A5 gene, TSHA-105 significantly lowered blood citrate levels and reduced seizures. SLC13A5 Citrate Transporter Disorder is a rare condition affecting brain development and causing seizures. This treatment targets the SLC13A5 gene, which facilitates the movement of citrate, an important molecule for energy production. Although research in humans is ongoing, early results from animal studies are encouraging.12367

Are You a Good Fit for This Trial?

This trial is for individuals with SLC13A5 Citrate Transporter Disorder. Specific eligibility criteria are not provided, but typically include factors like age range, disease severity, and overall health status.

Inclusion Criteria

Written informed consent provided by subject/parent/guardian and willingness to participate and comply with all the study related visits and procedures. Assent provided by children 10 to 17 years old based on their ability to understand the risks and possible benefits, and the activities expected of them
I have a confirmed SLC13A5 gene mutation causing my condition.
I have symptoms of SLC13A5 citrate transporter disorder.
See 2 more

Exclusion Criteria

I cannot undergo certain required procedures in this study.
I cannot take certain immune suppression medications.
I cannot have a lumbar puncture or use anesthetics due to another health issue.
See 11 more

Timeline for a Trial Participant

Screening

Participants are screened for eligibility to participate in the trial

2-4 weeks

Treatment

Single lumbar intrathecal administration of TSHA-105 to assess safety and efficacy

1 day
1 visit (in-person)

Follow-up

Participants are monitored for safety and effectiveness after treatment

5 years
Regular visits as per study protocol

What Are the Treatments Tested in This Trial?

Interventions

  • TSHA-105
Trial Overview The study is testing the efficacy and safety of TSHA-105 through a single lumbar intrathecal administration (an injection into the spinal canal) in patients with SLC13A5 Deficiency. It's an early-stage trial (Phase 1/2) that's open-label, meaning everyone knows they're getting the treatment.
How Is the Trial Designed?
1Treatment groups
Experimental Treatment
Group I: TSHA-105 treamentExperimental Treatment1 Intervention

Find a Clinic Near You

Who Is Running the Clinical Trial?

TESS Research Foundation

Lead Sponsor

Trials
2
Recruited
40+

Citations

Intrathecal Gene Therapy For SLC13A5 Citrate Transporter ...This clinical study is a pivotal open-label phase 1/2 study designed to assess safety and efficacy of TSHA-105 in individuals with SLC13A5 Citrate Transporter ...
Understanding SLC13A5SLC13A5 Epilepsy is a neurological disorder associated with the gene SLC13A5. This gene codes for a protein that is responsible for transporting citrate.
Taysha Gene TherapiesCSF-delivered TSHA-105 significantly decreased plasma citrate levels in SLC13A5 KO mice and reduced epileptic activity. Increased seizure ...
The growing research toolbox for SLC13A5 citrate transporter ...SLC13A5 citrate transporter disorder is an ultra-rare, neurodevelopmental disorder that severely impacts cognition and motor control. It is ...
SLC13A5 Gene and EpilepsyIn fact, a 2021 natural history study of 23 individuals with SLC13A5 variants found that all participants had seizures beginning in the neonatal ...
Taysha Gene Therapies Announces New Data on Multiple ...Positive proof-of-concept data for gene therapy candidates in SLC13A5 deficiency, APBD, Lafora disease and GM2 AB variant support advancement into clinical ...
TSHA-105 for SLC13A5 Deficiency · Info for ParticipantsTrial Overview The study is testing the efficacy and safety of TSHA-105 through a single lumbar intrathecal administration (an injection into the spinal canal) ...
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