Odevixibat for PFIC

Not currently recruiting at 49 trial locations
AP
Overseen ByAlbireo Pharma
Age: Any Age
Sex: Any
Trial Phase: Phase 3
Sponsor: Albireo, an Ipsen Company
No Placebo GroupAll trial participants will receive the active study treatment (no placebo)
Pivotal Trial (Near Approval)This treatment is in the last trial phase before FDA approval
Prior Safety DataThis treatment has passed at least one previous human trial

What You Need to Know Before You Apply

What is the purpose of this trial?

This trial tests the long-term safety and effectiveness of a new treatment called odevixibat for children with Progressive Familial Intrahepatic Cholestasis (PFIC), a rare liver condition. The medicine aims to manage symptoms such as severe itching and high bile acid levels in the blood. Participants will take capsules daily for 72 weeks. Children diagnosed with PFIC who experience significant itching or flare-ups might be suitable candidates for this study. As a Phase 3 trial, this study represents the final step before FDA approval, offering participants the opportunity to contribute to a potentially groundbreaking treatment.

Do I have to stop taking my current medications for the trial?

The trial protocol does not specify if you need to stop taking your current medications. However, it does exclude patients taking bile acid or lipid binding resins and medications that slow down gut movement.

Is there any evidence suggesting that A4250 (odevixibat) is likely to be safe for humans?

Research has shown that odevixibat, also known as A4250, is generally well tolerated by people with progressive familial intrahepatic cholestasis (PFIC), a rare liver disease. One study found that patients using odevixibat experienced ongoing improvements in their symptoms, with most not encountering serious side effects.

In this study, patients took odevixibat for an extended period, providing insight into its effectiveness in everyday life. Notably, odevixibat is already approved for another condition, offering some reassurance about its safety. Overall, current research supports the safety of odevixibat for people with PFIC, although individual experiences may vary.12345

Why do researchers think this study treatment might be promising for PFIC?

Unlike the standard treatments for Progressive Familial Intrahepatic Cholestasis (PFIC), which often involve surgical interventions or liver transplants, odevixibat offers a non-invasive option. Odevixibat is unique because it works by inhibiting the ileal bile acid transporter (IBAT), which reduces bile acid buildup in the liver. This new approach has the potential to alleviate symptoms and improve liver function without the need for surgery, making it an exciting development for both patients and researchers.

What evidence suggests that A4250 might be an effective treatment for PFIC?

Research has shown that odevixibat can help children with progressive familial intrahepatic cholestasis (PFIC), a rare liver disorder. Studies have found it reduces bile buildup in the liver and alleviates itching. Real-world experiences support these findings, demonstrating improvements in children with various types of PFIC. This suggests that odevixibat can ease symptoms and enhance the quality of life for those affected.23567

Who Is on the Research Team?

IM

Ipsen Medical Director

Principal Investigator

Ipsen

Are You a Good Fit for This Trial?

This trial is for children with PFIC, a liver disorder causing severe itching and jaundice. Participants need genetic confirmation of PFIC, have had significant pruritus, weigh at least 5 kg, and can use an eDiary. They must have completed or partially completed a prior A4250 study. Those with episodic PFIC should be experiencing a flare-up.

Inclusion Criteria

I have PFIC and have experienced significant itching, noted by myself or my caregiver.
I have PFIC with bile acid levels ≥100 μmol/L, confirmed by 2 tests.
I (or my guardian) have signed the consent form, and I will sign again if I turn 18 during the study.
See 9 more

Exclusion Criteria

Cohort 1: Patients not compliant with treatment in study A4250-005
Cohort 2: Total bilirubin >10 × ULN at Screening
I have a condition that affects how my body processes medication.
See 20 more

Timeline for a Trial Participant

Screening

Participants are screened for eligibility to participate in the trial

2-4 weeks

Treatment

Participants receive A4250 capsules for oral administration once daily

72 weeks
Regular visits as per study protocol

Follow-up

Participants are monitored for safety and effectiveness after treatment

4 weeks

Open-label extension

Participants continue to receive A4250 to evaluate long-term safety and efficacy

Long-term

What Are the Treatments Tested in This Trial?

Interventions

  • A4250 (odevixibat)
Trial Overview The trial tests the long-term safety and effectiveness of A4250 (odevixibat) in kids with PFIC. It's an open-label extension study meaning all participants receive the drug and are monitored over time to see how well it works and what side effects occur.
How Is the Trial Designed?
1Treatment groups
Experimental Treatment
Group I: A4250Experimental Treatment1 Intervention

Find a Clinic Near You

Who Is Running the Clinical Trial?

Albireo, an Ipsen Company

Lead Sponsor

Trials
5
Recruited
640+

Albireo

Lead Sponsor

Trials
17
Recruited
1,200+

Citations

Interim results from an ongoing, open-label, single-arm trial ...The current study, called PEDFIC 2, suggested that odevixibat can improve the problematic signs and symptoms of progressive familial intrahepatic cholestasis ...
NCT03659916 | Long Term Safety & Efficacy Study ...Study Overview. Brief Summary. Open Label Extension Study to evaluate long term safety and persistence of effect of A4250 in children with PFIC.
Real-world experience with odevixibat in children ...Our results demonstrate that odevixibat is effective for the treatment of cholestasis and pruritus in children with different PFIC subtypes in a real-life ...
Odevixibat (Bylvay) for the Treatment of Pruritus With ...Progressive familial intrahepatic cholestasis (PFIC) is a rare, autosomal recessive disease that results in impaired bile secretion and transport, leading to ...
NCT07185919 | A Study of the Effectiveness, Safety and ...This study will collect information from people with Progressive Familial Intrahepatic Cholestasis (PFIC) as they use odevixibat in their daily ...
PFIC Safety Profile | Bylvay® (odevixibat) HCP SiteData on file A4250-005. ... Interim results from an ongoing, open-label, single-arm trial of odevixibat in progressive familial intrahepatic cholestasis.
registry protocol a4250-019 - HMA-EMA CataloguesProgressive familial intrahepatic cholestasis (PFIC) is a group of rare genetic disorders that results from defects in bile secretion and presents with ...
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