FCX-007 for Epidermolysis Bullosa

(DEFI-RDEB Trial)

Not currently recruiting at 4 trial locations
Age: Any Age
Sex: Any
Trial Phase: Phase 3
Sponsor: Castle Creek Biosciences, LLC.
No Placebo GroupAll trial participants will receive the active study treatment (no placebo)
Pivotal Trial (Near Approval)This treatment is in the last trial phase before FDA approval
Prior Safety DataThis treatment has passed at least one previous human trial

What You Need to Know Before You Apply

What is the purpose of this trial?

This trial tests a new treatment called FCX-007, a gene therapy, to determine if it heals wounds more effectively than current methods for individuals with Recessive Dystrophic Epidermolysis Bullosa (RDEB). This rare skin condition causes fragile skin and painful blisters. Participants will receive injections directly into their wounds and will be compared to those receiving standard care. The trial seeks participants with a clinical diagnosis of RDEB and a specific genetic mutation (COL7A1). As a Phase 3 trial, this treatment represents the final step before FDA approval, offering hope for a new, effective therapy.

Will I have to stop taking my current medications?

The trial does not specify if you need to stop taking your current medications, but you cannot have received any chemical or biological treatment specifically for RDEB in the past three months before the study.

Is there any evidence suggesting that FCX-007 is likely to be safe for humans?

Research shows that FCX-007 looks promising based on earlier studies. Previous patients generally tolerated the treatment well. In one study, no serious side effects were directly linked to FCX-007. Most side effects were mild, such as temporary redness or swelling at the injection site.

This treatment uses the patient's own genetically modified cells to help lower the risk of severe reactions. Although the FDA has not yet approved it specifically for this condition, ongoing research suggests that the treatment could be safe for most people.12345

Why do researchers think this study treatment might be promising?

Unlike the standard treatments for Epidermolysis Bullosa, which often focus on symptom management, FCX-007 offers a new approach by using genetically-corrected autologous fibroblasts. This means it targets the root cause by correcting the faulty COL7A1 gene directly in the patient's skin cells. Researchers are excited because this method could potentially lead to lasting improvements in wound healing, offering hope for a more durable and effective solution to this challenging condition.

What evidence suggests that FCX-007 might be an effective treatment for Epidermolysis Bullosa?

Research has shown that FCX-007, a treatment using specially modified skin cells, offers potential benefits for people with Recessive Dystrophic Epidermolysis Bullosa (RDEB). In earlier studies, patients who received FCX-007 had higher levels of collagen VII, an important protein that strengthens skin, and experienced improved wound healing. These studies also found that the treatment helped form structures that hold skin layers together. The treatment was generally safe, with no major safety issues reported. These findings suggest that FCX-007 may effectively aid wound healing in people with RDEB. Participants in this trial will receive FCX-007 in specified treatment wounds, while control wounds will initially remain untreated.12345

Are You a Good Fit for This Trial?

This trial is for children and adults over 2 years old with Recessive Dystrophic Epidermolysis Bullosa (RDEB) confirmed by a specific genetic mutation. Participants must not have certain infections, antibodies, or cancer history at the treatment site, nor can they be pregnant or breastfeeding. They shouldn't have used other RDEB treatments in the last three months.

Inclusion Criteria

I am at least 2 years old.
I have RDEB confirmed by a COL7A1 genetic test.

Exclusion Criteria

You are allergic to any of the ingredients in the product.
My body has COL7 antibodies.
I have had squamous cell carcinoma where I will get injections.
See 6 more

Timeline for a Trial Participant

Screening

Participants are screened for eligibility to participate in the trial

2-4 weeks

Treatment

Participants receive intradermal injections of FCX-007 in treatment wounds during multiple sessions

12 months
Multiple visits at Day 1, Week 12, Week 24, and Week 36

Follow-up

Participants are monitored for safety and effectiveness after treatment

15 years

What Are the Treatments Tested in This Trial?

Interventions

  • FCX-007
Trial Overview The study tests if FCX-007 (dabocemagene autoficel), alongside usual care, improves wound healing compared to standard care alone in those with RDEB. The FDA's Office of Orphan Products Development funds this research.
How Is the Trial Designed?
1Treatment groups
Experimental Treatment
Group I: FCX-007 COL7A1 Genetically-Corrected Autologous FibroblastsExperimental Treatment1 Intervention

Find a Clinic Near You

Who Is Running the Clinical Trial?

Castle Creek Biosciences, LLC.

Lead Sponsor

Trials
12
Recruited
680+

Published Research Related to This Trial

In a phase I/IIa clinical trial involving 16 patients with recessive dystrophic epidermolysis bullosa (RDEB), treatment with ABCB5+ mesenchymal stem cells (MSCs) showed a statistically significant reduction in disease activity scores, indicating potential efficacy as a disease-modifying therapy.
The treatment was well-tolerated, with only three adverse events related to the cell product, all of which were manageable and resolved without lasting effects, suggesting a favorable safety profile for ABCB5+ MSCs.
Clinical trial of ABCB5+ mesenchymal stem cells for recessive dystrophic epidermolysis bullosa.Kiritsi, D., Dieter, K., Niebergall-Roth, E., et al.[2022]
Beremagene geperpavec (B-VEC) is a promising topical treatment for recessive dystrophic epidermolysis bullosa (RDEB), effectively restoring collagen VII (C7) expression and promoting wound healing in a clinical trial involving nine patients over 12 weeks.
The treatment was found to be safe, with no serious adverse events related to B-VEC, and it successfully met primary and secondary objectives related to wound healing and C7 expression.
In vivo topical gene therapy for recessive dystrophic epidermolysis bullosa: a phase 1 and 2 trial.Gurevich, I., Agarwal, P., Zhang, P., et al.[2022]

Citations

NCT04213261 | A Study of FCX-007 for Recessive ...The purpose of this study is to determine whether administration of FCX-007 in addition to standard of care improves wound healing as compared to standard of ...
Long-term safety and efficacy of gene-corrected autologous ...This Phase 1/2a, open-label study evaluated the long-term efficacy and safety of gene-corrected autologous keratinocyte grafts (EB-101) for chronic RDEB wounds.
NCT02810951 | A Study of FCX-007 for Recessive ...The purpose of this study is to evaluate the safety of FCX-007, evaluate Type VII collagen (COL7) expression and the presence of anchoring fibrils and to ...
Safety and early efficacy outcomes for lentiviral fibroblast gene ...Safety and wound outcomes following genetically corrected autologous epidermal grafts in patients with recessive dystrophic epidermolysis ...
A phase 1/2 study of genetically-corrected, collagen VII ...We report the results of the ongoing Phase 1/2 clinical trial of genetically-corrected, COL7 expressing autologous human dermal fibroblasts (FCX-007) for the ...
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