200 Participants Needed

Triple Therapy Modulator for Cystic Fibrosis

Recruiting at 18 trial locations
CB
EB
Overseen ByEvelyn Bord, BS
Age: Any Age
Sex: Any
Trial Phase: Academic
Sponsor: Boston Children's Hospital
Must be taking: VTD
No Placebo GroupAll trial participants will receive the active study treatment (no placebo)
Breakthrough TherapyThis drug has been fast-tracked for approval by the FDA given its high promise

What You Need to Know Before You Apply

What is the purpose of this trial?

This trial explores a new triple-therapy medication for individuals with Cystic Fibrosis (CF) who experienced mental health or liver issues with a previous treatment. The goal is to determine if the new drug combination (vanzacaftor, tezacaftor, deutivacaftor) is safe and effective for those who had to stop or change their old medication due to these side effects. Participants should have experienced new or worsening mental health symptoms or liver problems with the prior treatment and intend to start the new therapy. It suits those who can delay starting the new treatment and have a smart device to receive surveys. As a Phase 2 trial, this research focuses on measuring the treatment's effectiveness in an initial, smaller group, offering participants a chance to contribute to important CF advancements.

Do I need to stop my current medications to join the trial?

The trial does not specify if you need to stop your current medications. However, it mentions that participants should be willing to delay the first dose of the new treatment for a short period to complete baseline assessments.

Is there any evidence suggesting that this trial's treatments are likely to be safe?

Research has shown that the medication vanzacaftor-tezacaftor-deutivacaftor (VTD) is safe and well tolerated for people with cystic fibrosis. Studies have found that it works as effectively as another treatment, elexacaftor-tezacaftor-ivacaftor (ETI), improving lung function and other symptoms.

Trials have proven VTD safe and effective for children as young as 6 years old and for older patients, ages 12 and up. People taking VTD generally did not experience more side effects than those taking ETI.

For those concerned about side effects, it is reassuring that VTD has undergone testing for long-term safety. Researchers are closely monitoring any potential issues, and so far, the treatment is considered safe for people with cystic fibrosis.12345

Why are researchers excited about this trial?

Researchers are excited about the new combination of vanzacaftor/tezacaftor/deutivacaftor (VTD) because it offers potential benefits for people with cystic fibrosis (CF) who experience side effects from the current standard treatment, elexacaftor/tezacaftor/ivacaftor (ETI). The VTD combination is being explored for its ability to reduce mental health and neurocognitive symptoms, like depression and brain fog, which some patients experience on ETI. Additionally, VTD may offer a safer profile for individuals who have had drug-induced liver issues with ETI, potentially lowering the risk of liver injury. This makes VTD an exciting prospect as it could provide a more tolerable and effective treatment option for individuals with challenging side effects from existing therapies.

What evidence suggests that this trial's treatments could be effective for Cystic Fibrosis?

This trial will evaluate the treatment vanzacaftor-tezacaftor-deutivacaftor (VTD) for cystic fibrosis in various contexts. Research has shown that VTD is promising for cystic fibrosis, with studies indicating it matches elexacaftor-tezacaftor-ivacaftor (ETI) in improving lung function for individuals aged 12 and older. It is also safe and effective for children aged 6 to 11. Participants in the RETRIAL-Mental Health arm will include those with a history of mental health symptoms while on ETI. The RETRIAL-Neuro arm will focus on individuals with neurocognitive symptoms, and the RETRIAL-Liver arm will include participants with liver-related issues attributed to ETI. While ETI can sometimes cause liver problems, VTD might offer a safer option with fewer liver-related side effects. Overall, VTD is well-tolerated and effective for managing cystic fibrosis.36789

Who Is on the Research Team?

AG

Anna Georgiopoulos, MD

Principal Investigator

Massachusetts General Hospital

CB

CJ Bathgate, PhD

Principal Investigator

National Jewish Health

JS

Janis Stoll, MD

Principal Investigator

Washington University at St. Louis

Are You a Good Fit for This Trial?

Inclusion Criteria

I am eligible for VTD treatment.
I am not taking any modulators.
I am not taking ETI as a modulator.
See 7 more

Timeline for a Trial Participant

Screening

Participants are screened for eligibility to participate in the trial

2-4 weeks

Treatment

Participants start taking vanzacaftor/tezacaftor/deutivacaftor (VTD) and are monitored for mental health and liver-related adverse events

12 months
Biweekly visits for the first 6 months, followed by visits at 9 and 12 months

Follow-up

Participants are monitored for safety and effectiveness after treatment

4 weeks

What Are the Treatments Tested in This Trial?

Interventions

  • Vanzacaftor/Tezacaftor/Deutivacaftor (VTD)

How Is the Trial Designed?

3

Treatment groups

Experimental Treatment

Group I: RETRIAL-NeuroExperimental Treatment1 Intervention
Group II: RETRIAL-Mental HealthExperimental Treatment1 Intervention
Group III: RETRIAL-LiverExperimental Treatment1 Intervention

Find a Clinic Near You

Who Is Running the Clinical Trial?

Boston Children's Hospital

Lead Sponsor

Trials
801
Recruited
5,584,000+

Cystic Fibrosis Foundation

Collaborator

Trials
199
Recruited
37,800+

National Jewish Health

Collaborator

Trials
145
Recruited
318,000+

Washington University School of Medicine

Collaborator

Trials
2,027
Recruited
2,353,000+

Massachusetts General Hospital

Collaborator

Trials
3,066
Recruited
13,430,000+

University of Kansas Medical Center

Collaborator

Trials
527
Recruited
181,000+

Johns Hopkins University

Collaborator

Trials
2,366
Recruited
15,160,000+

Children's Hospital Colorado

Collaborator

Trials
121
Recruited
5,135,000+

Indiana University

Collaborator

Trials
1,063
Recruited
1,182,000+

Citations

Vanzacaftor–tezacaftor–deutivacaftor versus elexacaftor– ...

These results show that vanzacaftor–tezacaftor–deutivacaftor treatment might lead to more people with cystic fibrosis attaining levels of CFTR function either ...

2.

alyftrekhcp.com

alyftrekhcp.com/trial-3

Trial 3 | ALYFTREK® (vanzacaftor/tezacaftor/deutivacaftor)

One patient had 2 serious adverse events: infective pulmonary exacerbation of cystic fibrosis and failure to thrive. 2. Liver function test elevations1,4 ...

Study Results

TRIKAFTA can cause serious liver damage and liver failure. Liver failure leading to transplantation and death has been seen in some people with or without a ...

Vertex Presents New Data Across Portfolio of Cystic ...

TRIKAFTA can cause serious and potentially fatal drug-induced liver injury. ... Liver injury has been reported within the first month of therapy ...

Evaluation of Long-Term Safety and Efficacy of Vanzacaftor ...

The purpose of this study is to evaluate the long-term safety, tolerability, and efficacy of vanzacaftor / tezacaftor / deutivacaftor (VNZ/TEZ/D-IVA) in ...

6.

pubmed.ncbi.nlm.nih.gov

pubmed.ncbi.nlm.nih.gov/39756425/

Vanzacaftor-tezacaftor-deutivacaftor for children aged 6-11 ...

Vanzacaftor-tezacaftor-deutivacaftor has been shown to be a safe and effective, once-daily cystic fibrosis transmembrane conductance regulator (CFTR) modulator.

Safety and efficacy of vanzacaftor–tezacaftor–deutivacaftor ...

Elexacaftor–tezacaftor–ivacaftor has been shown to be safe and efficacious in people with cystic fibrosis and at least one F508del allele.

Vanzacaftor–Tezacaftor–Deutivacaftor Noninferior to ETI

Vanzacaftor–tezacaftor–deutivacaftor was noninferior to elexacaftor–tezacaftor–ivacaftor among patients aged 12 years and older with cystic fibrosis.

9.

pubmed.ncbi.nlm.nih.gov

pubmed.ncbi.nlm.nih.gov/39756424/

Vanzacaftor-tezacaftor-deutivacaftor versus elexacaftor ...

Vanzacaftor-tezacaftor-deutivacaftor is non-inferior to elexacaftor-tezacaftor-ivacaftor in terms of FEV 1 % predicted, and is safe and well tolerated.