Molgramostim for Pulmonary Alveolar Proteinosis

YW
RD
Overseen ByRaymond D Pratt, MD
Age: < 65
Sex: Any
Trial Phase: Phase 3
Sponsor: Savara Inc.
Must be taking: Molgramostim
No Placebo GroupAll trial participants will receive the active study treatment (no placebo)
Pivotal Trial (Near Approval)This treatment is in the last trial phase before FDA approval
Prior Safety DataThis treatment has passed at least one previous human trial

What You Need to Know Before You Apply

What is the purpose of this trial?

This trial tests molgramostim as a treatment for autoimmune pulmonary alveolar proteinosis (aPAP) in children and teenagers. Researchers aim to determine if molgramostim improves breathing and activity levels and assess its safety. Participants will use molgramostim daily through a nebulizer for about a year and monitor their oxygen use. This trial may suit young individuals diagnosed with aPAP who experience lung function difficulties. As a Phase 3 trial, it represents the final step before FDA approval, allowing participants to contribute to a potentially groundbreaking treatment.

Do I need to stop my current medications for this trial?

The trial information does not specify whether you need to stop taking your current medications. It's best to discuss this with the trial coordinators or your doctor.

Is there any evidence suggesting that molgramostim is likely to be safe for pediatric patients with aPAP?

Research has shown that molgramostim is generally well-tolerated by people with autoimmune pulmonary alveolar proteinosis (aPAP). One study found that the most common side effects were cough and a cold-like nose and throat infection, affecting about 11.9% of patients. Other side effects, such as respiratory infections, joint pain, and COVID-19, occurred less frequently.

Although the treatment is still under investigation, its late-stage trial status indicates some evidence of safety. This suggests it could be a manageable option for those considering joining the trial.12345

Why do researchers think this study treatment might be promising for aPAP?

Unlike the standard treatments for pulmonary alveolar proteinosis, which often involve whole lung lavage or GM-CSF injections, molgramostim is administered as a daily nebulized therapy. This delivery method allows for direct targeting of the lungs, potentially increasing efficacy and reducing systemic side effects. Researchers are excited about molgramostim because it combines an innovative delivery system with the active ingredient GM-CSF, aiming to improve lung function more conveniently and comfortably for patients.

What evidence suggests that molgramostim might be an effective treatment for aPAP?

Research has shown that molgramostim, the treatment under study in this trial, can improve lung function in people with autoimmune pulmonary alveolar proteinosis (aPAP). In earlier studies, patients using molgramostim demonstrated better lung performance, measured by gas transfer efficiency, compared to those on a placebo. Specifically, lung function improved by 11.6% after 48 weeks of treatment. Additionally, molgramostim was well tolerated, with no serious side effects reported. These findings suggest that molgramostim could effectively treat people with aPAP.46789

Who Is on the Research Team?

YW

Yasmine Wasfi, MD, Ph.D.

Principal Investigator

Savara Inc.

Are You a Good Fit for This Trial?

This trial is for children aged 6-18 with autoimmune pulmonary alveolar proteinosis (aPAP), a rare lung disease. Participants must be able to use a nebulizer daily and visit the clinic every 12 weeks. Specific eligibility criteria are not provided, but typically include having the condition being studied and meeting certain health requirements.

Inclusion Criteria

I have been diagnosed with pulmonary alveolar proteinosis.
I am between 6 and 17 years old.
I tested positive for aPAP.
See 1 more

Exclusion Criteria

I had a lung lavage treatment within the last month.
I have a genetic or acquired lung condition affecting surfactant.

Timeline for a Trial Participant

Screening

Participants are screened for eligibility to participate in the trial

4 weeks

Treatment

Participants receive molgramostim once daily via nebulizer for 48 weeks

48 weeks
Clinic visits approximately every 12 weeks

Follow-up

Participants are monitored for safety and effectiveness after treatment

4 weeks

What Are the Treatments Tested in This Trial?

Interventions

  • Molgramostim
Trial Overview The study tests molgramostim, an inhaled medication delivered via nebulizer, as a treatment for pediatric aPAP. Over 12 months, all participants will receive this drug daily to assess its impact on breathing function and activity levels without comparing it to another drug or placebo.
How Is the Trial Designed?
1Treatment groups
Experimental Treatment
Group I: molgramostimExperimental Treatment1 Intervention

Find a Clinic Near You

Who Is Running the Clinical Trial?

Savara Inc.

Lead Sponsor

Trials
11
Recruited
750+

Published Research Related to This Trial

A young man with pulmonary alveolar proteinosis achieved complete remission after being treated with granulocyte-macrophage colony stimulating factor (GM-CSF), suggesting it as a promising new treatment option.
This case highlights the potential of GM-CSF as an alternative to the traditional whole lung lavage treatment for this rare condition.
Pulmonary alveolar proteinosis: a complete response to GM-CSF therapy.Barraclough, RM., Gillies, AJ.[2019]

Citations

1.pubmed.ncbi.nlm.nih.govpubmed.ncbi.nlm.nih.gov/40834301/
Phase 3 Trial of Inhaled Molgramostim in Autoimmune ...Conclusions: Once-daily inhaled molgramostim led to a greater increase in pulmonary gas transfer than placebo in patients with aPAP. (Funded by ...
Savara Presents New Data From the Phase 3 IMPALA-2 ...Molgramostim demonstrated improvement compared with placebo on the primary endpoint, change in DLco% from baseline to Week 24, in patients with ...
Long-term outcomes in five patients with autoimmune ...There were no reported serious adverse events in these five patients while receiving molgramostim and the treatment has been well tolerated. TABLE 1.
results from the IMPALA-2 phase 3 clinical trialMolgramostim was well tolerated and improved pulmonary gas exchange, respiratory health-related quality of life, and EC of patients with aPAP.
Phase 3 Drug Trial Shows Lung Function Improvement for ...After 48 weeks of daily doses, study participants receiving molgramostim saw an 11.6% improvement in pulmonary gas transfer compared to 4.7% ...
Safety and Tolerability of Inhaled Molgramostim in ...aPAP is a rare lung disease characterized by the accumulation of lipoproteinaceous surfactant material in the alveoli of the lungs leading to respiratory ...
Safety and tolerability of inhaled molgramostim in autoimmune ...Most common AEs (7 patients each, 11.9%) were cough and nasopharyngitis. Respiratory tract infection, arthralgia, alveolar proteinosis, and COVID-19 were each ...
Study Details | NCT03482752 | Safety Extension Trial of ...An open-label, non-controlled, multicentre clinical trial of inhaled molgramostim in autoimmune pulmonary alveolar proteinosis.
Safety and Efficacy of Inhaled GM-CSF (Molgramostim) in ...Background: Autoimmune Pulmonary Alveolar Proteinosis (aPAP). • aPAP is characterized by: – Pulmonary surfactant accumulation.
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