30 Participants Needed

Asfotase Alfa for Hypophosphatasia

Recruiting at 19 trial locations
AP
AP
Overseen ByAlexion Pharmaceuticals, Inc. (Sponsor)
Age: Any Age
Sex: Any
Trial Phase: Academic
Sponsor: Alexion Pharmaceuticals, Inc.
Must be taking: Asfotase alfa
No Placebo GroupAll trial participants will receive the active study treatment (no placebo)
Breakthrough TherapyThis drug has been fast-tracked for approval by the FDA given its high promise

What You Need to Know Before You Apply

What is the purpose of this trial?

This trial observes individuals with pediatric-onset hypophosphatasia (HPP) who are receiving or will soon begin treatment with asfotase alfa, a medication designed to manage this rare bone disease. The researchers aim to assess how the treatment affects various aspects of health and quality of life over at least five years. Individuals who showed symptoms of HPP before age 18 and are either currently on asfotase alfa or plan to start it soon are eligible. Participants must also have low levels of a specific enzyme related to HPP. As a Phase 4 trial, this study focuses on understanding how the already FDA-approved and effective treatment benefits more patients, providing valuable insights into long-term health improvements.

Do I have to stop taking my current medications for this trial?

The trial information does not specify whether you need to stop taking your current medications. However, you must be receiving or planning to start asfotase alfa treatment.

What prior data suggests that Asfotase Alfa is safe for pediatric-onset hypophosphatasia?

Research has shown that Asfotase Alfa is usually well-tolerated. Most patients experience only mild side effects, such as redness or swelling at the injection site. Some may also experience headaches or a fever.

The FDA has already approved the treatment for a different condition, indicating that its safety is well understood. This approval helps doctors understand its effects on the body and potential side effects. However, individual responses can vary, so discussing any concerns with a doctor is important.

Why are researchers excited about this trial?

Unlike traditional treatments for hypophosphatasia (HPP), which often focus on managing symptoms, Asfotase Alfa targets the root cause of the disease. It is an enzyme replacement therapy designed to address the enzyme deficiency that leads to HPP. Researchers are excited about Asfotase Alfa because it has the potential to significantly improve bone mineralization and overall quality of life for patients, particularly those with pediatric-onset HPP. This targeted approach distinguishes it from standard treatments and offers new hope for a more effective management strategy.

What evidence suggests that Asfotase Alfa might be an effective treatment for hypophosphatasia?

Research has shown that asfotase alfa helps manage symptoms of hypophosphatasia (HPP), a rare bone disease. Studies have found that children taking asfotase alfa experience better growth, with improvements in height and weight. For adults with childhood-onset HPP, asfotase alfa enhances physical abilities and quality of life. Long-term evidence supports that this treatment manages various HPP symptoms over many years. Overall, asfotase alfa has a strong record of improving life for those with childhood-onset HPP.12345

Are You a Good Fit for This Trial?

Inclusion Criteria

Currently receiving asfotase alfa treatment at Enrollment (not treatment-naïve) or the Physician has decided to resume (not treatment-naïve) or start (treatment-naïve) the participant's asfotase alfa treatment within 6 months after Enrollment.
Participant must have documented alkaline phosphatase (ALP) activity below the lower limit of normal for age and sex, and a documented ALPL gene mutation (Note: An exception is made for infants with clinical features of HPP plus low ALP who need to start asfotase alfa treatment right away, at the Physician's discretion, but do not yet have a genetic result. In this case, ALPL gene documentation is not required at the time of sub-study enrollment but should be documented within 6 months after Enrollment).
Participant or participant's parent/legally authorized representative is able to read and/or understand the informed consent and study questionnaires in the local language.
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Timeline for a Trial Participant

Screening

Participants are screened for eligibility to participate in the trial

2-4 weeks

Observational Follow-up

Participants with pediatric-onset hypophosphatasia are followed for a minimum of 5 years to assess biochemical, clinical, imaging, and functional/quality of life outcomes

5 years

Follow-up

Participants are monitored for safety and effectiveness after the observational period

6 months

What Are the Treatments Tested in This Trial?

Interventions

  • Asfotase Alfa

How Is the Trial Designed?

1

Treatment groups

Experimental Treatment

Group I: Participants with Pediatric-onset HPPExperimental Treatment1 Intervention

Find a Clinic Near You

Who Is Running the Clinical Trial?

Alexion Pharmaceuticals, Inc.

Lead Sponsor

Trials
267
Recruited
141,000+
Dr. Alberto R. Martinez profile image

Dr. Alberto R. Martinez

Alexion Pharmaceuticals, Inc.

Chief Medical Officer since 2010

MD from University of Sao Paulo

Marc Dunoyer profile image

Marc Dunoyer

Alexion Pharmaceuticals, Inc.

Chief Executive Officer since 2021

PhD in Molecular Biology

Alexion

Lead Sponsor

Trials
247
Recruited
38,600+
Marc Dunoyer profile image

Marc Dunoyer

Alexion

Chief Executive Officer since 2021

PhD in Molecular Biology, University of Brussels

Christophe Hotermans profile image

Christophe Hotermans

Alexion

Chief Medical Officer since 2021

MD, University of Leuven

Alexion Pharmaceuticals

Lead Sponsor

Trials
231
Recruited
36,700+
Marc Dunoyer profile image

Marc Dunoyer

Alexion Pharmaceuticals

Chief Executive Officer since 2021

B.A. in Psychology from the University of New Hampshire

Christophe Hotermans profile image

Christophe Hotermans

Alexion Pharmaceuticals

Chief Medical Officer since 2023

MD

Citations

1.

pubmed.ncbi.nlm.nih.gov

pubmed.ncbi.nlm.nih.gov/40439960/

Mobility and Quality of Life in Children with Paediatric ...

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This study of a real-world cohort of adults with pediatric-onset HPP suggests that asfotase alfa is effective in improving physical functioning, fatigue, sleep, ...

10 Years Post-Approval | Advances in Therapy

The findings from the past decade show that asfotase alfa is effective in managing the wide range of symptoms associated with hypophosphatasia, ...

Long-term effectiveness of asfotase alfa in adults with ...

These data suggest adults who have pediatric-onset HPP treated with asfotase alfa in real-world settings have marked improvements in clinical and functional ...